Product Name :
delta Sarcoglycan Recombinant Rabbit Monoclonal Antibody [JM61-10]
Predicted band size :
Observed band size :
Synonyms:
35 kDa dystrophin associated glycoprotein antibody 35 kDa dystrophin-associated glycoprotein antibody 35DAG antibody CMD1L antibody DAGD antibody Delta-sarcoglycan antibody Delta-SG antibody Dystrophin associated glycoprotein delta sarcoglycan antibody LGMD2F antibody MGC22567 antibody 展开
Function :
Component of the sarcoglycan complex, a subcomplex of the dystrophin-glycoprotein complex which forms a link between the F-actin cytoskeleton and the extracellular matrix. Defects in SGCD are the cause of limb-girdle muscular dystrophy type 2F (LGMD2F) [MIM:601287]. LGMD2F is an autosomal recessive disorder. Defects in SGCD are the cause of cardiomyopathy dilated type 1L (CMD1L) [MIM:606685]. Dilated cardiomyopathy is a disorder characterized by ventricular dilation and impaired systolic function, resulting in congestive heart failure and arrhythmia.4-(Methylamino)butan-1-ol Price Patients are at risk of premature death.
Antibody Type:
Recombinant Rabbit monoclonal Antibody
Immunogen :
Synthetic peptide within Human delta Sarcoglycan aa 221-265 / 289.
Species reactivity:
Human
Verify application:
WB, IP, IHC-P
Coupling :
unconjugated
Clone number:
JM61-10
RRID:
AB_3070442
Form :
Liquid
Concentration :
1ug/ul
Storage instructions:
Store at +4℃ after thawing.Price of 5-Bromo-4-chloro-2-methylpyrimidine Aliquot store at -20℃ or -80℃.PMID:33576270 Avoid repeated freeze / thaw cycles.
Storage buffer solution:
1*TBS (pH7.4), 0.05% BSA, 40% Glycerol. Preservative: 0.05% Sodium Azide.
Subtype:
IgG
Purification method :
Protein A affinity purified.
ELTSA :
Molecular weight :
32 kDa
Positive control :
Human lung tissue lysate, human skeletal muscle tissue lysate, human stomach carcinoma tissue.